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STUDIES ON LIVER ARGININOSUCCINATE SYNTHETASE IN A PATIENT WITH CITRULLINEMIA AND IN NORMAL SUBJECTSMATSUDA Y; TSUJI A; KATUNUMA N et al.1979; J. BIOCHEM.; JPN; DA. 1979; VOL. 85; NO 1; PP. 191-195; BIBL. 18 REF.Article

STUDIES ON COMPLEMENTATION IN ARGININOSUCCINATE SYNTHETASE AND ARGININOSUCCINATE LYASE DEFICIENCIES IN HUMAN FIBROBLASTSCATHELINEAU L; PHAM DINH D; BRIAND P et al.1981; HUM. GENET.; ISSN 0340-6717; DEU; DA. 1981; VOL. 57; NO 3; PP. 282-284; BIBL. 18 REF.Article

ETUDES SUR L'ETIOLOGIE DE L'HYPERAMMONIEMIE LIEE AUX ERREURS INNEES DU METABOLISME DES ACIDES AMINES. I. ETIOLOGIE DE L'HYPERAMMONIEMIE LIEE AUX TROUBLES DU METABOLISME DE LA LYSINESOGAWA H.1978; SAPPORO MED. J.; JPN; DA. 1978; VOL. 47; NO 2; PP. 204-214; ABS. ENG; BIBL. 1 P. 1/2Article

CONTROL OF ARGININOSUCCINATE SYNTHETASE BY ARGININE IN HUMAN LYMPHOBLASTS.IRR JD; JACOBY LB.1978; SOMAT. CELL GENET.; USA; DA. 1978; VOL. 4; NO 1; PP. 111-124; BIBL. 17 REF.Article

CITRULLINEMIA, ARGININOSUCCINATE SYNTHETASE DEFICIENCY. REPOSITORY IDENTIFICATION NO GM-1044.SPECTOR E; KENNAWAY N; PUNNETT H et al.1977; CYTOGENET. CELL GENET.; SWITZ.; DA. 1977; VOL. 19; NO 1; PP. 51-52; BIBL. 4 REF.Article

EFFECT OF DIETARY PROTEINS ON THE TURNOVER OF RAT LIVER ARGININOSUCCINATE SYNTHETASETSUDA M; SHIKATA Y; KATSUNUMA T et al.1979; J. BIOCHEM.; JPN; DA. 1979; VOL. 85; NO 3; PP. 699-704; BIBL. 15 REF.Article

STUDIES ON RAT LIVER ARGININOSUCCINATE SYNTHETASE. INHIBITION BY VARIOUS AMINO ACIDSTAKADA S; SAHEKI T; IGARASHI Y et al.1979; J. BIOCHEM.; JPN; DA. 1979; VOL. 85; NO 5; PP. 1309-1314; BIBL. 16 REF.Article

Molecular structures of human argininosuccinate synthetase pseudogenes: evolutionary and mechanistic implicationsFREYTAG, S. O; BOCK, H.-G. O; BEAUDET, A. L et al.The Journal of biological chemistry (Print). 1984, Vol 259, Num 5, pp 3160-3166, issn 0021-9258Article

Immunohistochemical localization of argininosuccinate synthetase in the rat brain in relation to nitric oxide synthase-containing neuronsARNT-RAMOS, L. R; O'BRIEN, W. E; VINCENT, S. R et al.Neuroscience. 1992, Vol 51, Num 4, pp 773-789, issn 0306-4522Article

DETOXICATION OF AMMONIA BY IMMOBILIZED UREA CYCLE ENZYMES = DETOXICATION DE L'AMMONIAQUE PAR LES ENZYMES DU CYCLE DE L'UREE IMMOBILISEESMIURA Y; URABE H; MIYAMOTO K et al.1980; ENZYME ENGINEERING. INTERNATIONAL ENZYME ENGINEERING CONFERENCE. 5/1979-07-29/HENNIKER NH; USA/GBR; NEW YORK; LONDON: PLENUM PRESS; DA. 1980; PP. 247-250; BIBL. 5 REF.Conference Paper

DOUBLE DEFICIENCIES OF UREA CYCLE ENZYMES IN HUMAN LIVERRAIJMAN L.1979; BIOCHEM. MED.; USA; DA. 1979; VOL. 21; NO 2; PP. 226-233; BIBL. 14 REF.Article

Immunocytochemical localization of argininosuccinate synthetase in the rat brainNAKAMURA, H; SAHEKI, T; ICHIKI, H et al.Journal of comparative neurology (1911). 1991, Vol 312, Num 4, pp 652-679, issn 0021-9967Article

Heterogeneity of mutations in argininosuccinate synthetase causing human citrullinemiaKOBAYASHI, K; JACKSON, M. J; TICK, D. B et al.The Journal of biological chemistry (Print). 1990, Vol 265, Num 19, pp 11361-11367, issn 0021-9258, 7 p.Article

Lysinuric protein intolerance presenting deficiency of argininosuccinate synthetaseONO, N; KISHIDA, K; TOKUMOTO, K et al.Internal medicine : (Tokyo). 1992, Vol 31, Num 1, pp 55-59Article

Immunocytochemical demonstration of argininosuccinate synthetase in the neuronal structures of the intestinal tract and pancreas of the Japanese monkeyNAKAGAWA, S; MIZUMA, M; ICHIKI, H et al.Acta histochemica et cytochemica. 1991, Vol 24, Num 2, pp 209-213, issn 0044-5991Article

Detection of kinetically abnormal arginisocuccinate synthase in neonatal citrullinemia by conversion of citrulline to arginine in intact fibroblastsBEN-YOSEPH, Y; MITCHELL, D. A.Clinica chimica acta. 1989, Vol 183, Num 2, pp 125-134, issn 0009-8981, 10 p.Article

YEAST ARGININOSUCCINATE SYNTHETASE: PURIFICATION; STRUCTURAL AND KINETIC PROPERTIESHILGER F; SIMON JP; STALON V et al.1979; EUROP. J. BIOCHEM.; DEU; DA. 1979; VOL. 94; NO 1; PP. 153-163; BIBL. 31 REF.Article

CITRULLINEMIE: FORME NEO-NATALE SEVERE. REVUE DE LA LITTERATURE. A PROPOS D'UN CASPLASSE MIREILLE.1978; ; FRA; DA. 1978; 129; 140 P.; 30 CM; BIBL. 71 REF.; TH.: MED./GRENOBLE 1/1978Thesis

SOMATIC CELL GENETIC EVIDENCE FOR THE PRESENCE OF A GENE FOR CITRULLINEMIA ON HUMAN CHROMOSOME 9.CARRITT B.1977; CYTOGENET. CELL GENET.; SWITZ.; DA. 1977; VOL. 19; NO 1; PP. 44-48; BIBL. 7 REF.Article

STUDIES OF RAT LIVER ARGININOSUCCINATE SYNTHETASE. I. PHYSICOCHEMICAL, CATALYTIC, AND IMMUNOCHEMICAL PROPERTIES.SAHEKI T; KUSUMI T; TAKADA S et al.1977; J. BIOCHEM.; JAP.; DA. 1977; VOL. 81; NO 3; PP. 687-696; BIBL. 26 REF.Article

ARGININOSUCCINATE SYNTHETASE ACTIVITY IN CULTURED HUMAN LYMPHOCYTES.LOCKRIDGE O; SPECTOR EB; BLOOM AD et al.1977; BIOCHEM. GENET.; U.S.A.; DA. 1977; VOL. 15; NO 3-4; PP. 395-407; BIBL. 19 REF.Article

BIOSYNTHESIS OF UREA. MOLECULAR AND REGULATORY PROPERTIES OF CRYSTALLINE ARGININOSUCCINATE SYNTHETASE.ROCHOVANSKY O; KODOWAKI H; RATNER S et al.1977; J. BIOL. CHEM.; U.S.A.; DA. 1977; VOL. 252; NO 15; PP. 5287-5294; BIBL. 23 REF.Article

ISOLATION AND CHARACTERIZATION OF ARGININOSUCCINATE SYNTHETASE FROM HUMAN LIVERO'BRIEN WE.1979; BIOCHEMISTRY; USA; DA. 1979; VOL. 18; NO 24; PP. 5353-5356; BIBL. 31 REF.Article

NEW RADIOISOTOPIC ASSAYS FOR ARGININOSUCCINATE SYNTHETASE AND ARGININOSUCCINASE.KATO H; OYAMADA I; MIZUTANI FUNAHASHI M et al.1976; J. BIOCHEM.; JAP.; DA. 1976; VOL. 79; NO 5; PP. 945-953; BIBL. 22 REF.Article

INTRAZELLULAERE LOKALISATION VON ENZYMEN DES KREBS-HENSELEIT-CYCLUS IN DER LEBER. = LOCALISATION INTRACELLULAIRE, DANS LE FOIE, DES ENZYMES DU CYCLE DE KREBS-HENSELEITMAIER KP; TALKE H; HOPPE SEYLER G et al.1976; KLIN. WSCHR.; DTSCH.; DA. 1976; VOL. 54; NO 21; PP. 1021-1025; ABS. ANGL.; BIBL. 20 REF.Article

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